Open fontanelle is a soft spot located on top of the head in a newborn due to incomplete fusion of the cranial bones. They are the normal structure in young puppies, especially in small breeds and get hardened by 9-12 weeks of age following fusion of growth plates in the skull. The aim of our study was to describe the presence, diagnosis and management of open fontanelle. A puppy was presented with the history of swelling over the frontal region, intermittent seizures for the past two weeks. Clinical examination revealed a swelling over the mid-frontal region of head. Radiographic examination of skull revealed hydrocephalus with open fontanelle.